Table 3

Diagnostic criteria for long QT syndrome (the Schwartz score)

Diagnostic criteriaPoints
ECG findingsQTc calculated by Bazett's formula*≥480 ms3
460–470 ms2
450 ms (males)1
Torsades de pointes2
T wave alternans1
Notched T wave in three leads1
Resting heart rate below second centile for age0.5
Clinical historySyncopeWith stress2
Without stress1
Congenital deafness0.5
Family historyFamily members with definite LQTS by Schwartz score1
Immediate family members with SCD <30 years old0.5
  • Score ≤1, low probability of LQTS; 2–3, intermediate probability of LQTS; ≥4, high probability of LQTS.

  • * In the absence of drugs or disorders known to affect QTc.

  • Mutually exclusive.

  • The same family member cannot be counted in both family history categories.

  • LQTS, long QT syndrome; QTc, corrected QT interval; SCD, sudden cardiac death.